Clinical Practice Guideline: Adult Congenital Heart Disease (ACHD)

Brief Description

•Congenital heart disease (CHD) is the most common birth defect, occurring in ~1% of births. With improved survival rates, there are now over 1.5 million adults in the US living with repaired or unrepaired CHD.

•ACHD patients are at risk for cardiovascular and systemic complications, such as: cardiomyopathy (HFpEF and HFrEF), right heart failure, pulmonary arterial hypertension, valvular heart disease, atrial and ventricular arrhythmias, and chronic lung or kidney disease.

•The 2018 AHA/ACC Guideline for Management of ACHD classifies congenital heart disease by both anatomy and physiology (Appendix A).

•Patients with severe anatomic forms of CHD, reduced functional status, and significant co-morbidities are at greater risk for complications.

•For COVID-19 Considerations in patients with ACHD, see Patients with COVID-19 and Appendix B.